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Fatty acid composition of free ceramides of kidney and cerebellum from a patient with Farber's disease.

作者信息

Sugita M, Connolly P, Dulaney J T, Moser H W

出版信息

Lipids. 1973 Jul;8(7):401-6. doi: 10.1007/BF02531715.

DOI:10.1007/BF02531715
PMID:4740649
Abstract
摘要

相似文献

1
Fatty acid composition of free ceramides of kidney and cerebellum from a patient with Farber's disease.法伯病患者肾脏和小脑游离神经酰胺的脂肪酸组成。
Lipids. 1973 Jul;8(7):401-6. doi: 10.1007/BF02531715.
2
High performance liquid chromatography of ceramides: application to analysis in human tissues and demonstration of ceramide excess in Farber's disease.神经酰胺的高效液相色谱法：在人体组织分析中的应用及法伯病中神经酰胺过量的证明
J Lipid Res. 1974 May;15(3):223-6.
3
Ceramides in a patient with lipogranulomatosis (Farber's disease) with chronic course.一名患有慢性病程的脂肪肉芽肿病（法伯病）患者体内的神经酰胺
Scand J Clin Lab Invest. 1971 Jun;27(4):393-405. doi: 10.3109/00365517109080235.
4
Ceramidase deficiency in Farber's disease (lipogranulomatosis).法伯病（脂肪肉芽肿病）中的神经酰胺酶缺乏症。
Science. 1972 Dec 8;178(4065):1100-2. doi: 10.1126/science.178.4065.1100.
5
Ceramidase and ceramide synthesis in human kidney and cerebellum. Description of a new alkaline ceramidase.人肾和小脑中的神经酰胺酶与神经酰胺合成。一种新型碱性神经酰胺酶的描述。
Biochim Biophys Acta. 1975 Jul 22;398(1):125-31. doi: 10.1016/0005-2760(75)90176-9.
6
Above-normal urinary excretion of urinary ceramides in Farber's disease, and characterization of their components by high-performance liquid chromatography.法布里病患者尿神经酰胺排泄高于正常水平及其成分的高效液相色谱表征
Clin Chem. 1975 May;21(6):725-9.
7
Farber's lipogranulomatosis. Report of a case and demonstration of an excess of free ceramide and ganglioside.法伯尔脂肪肉芽肿病。一例报告及游离神经酰胺和神经节苷脂过量的证明。
Am J Med. 1969 Dec;47(6):869-90. doi: 10.1016/0002-9343(69)90202-2.
8
Farber's disease as a ceramidosis: clinical, radiological and biochemical aspects.法伯病作为一种神经酰胺沉积症：临床、放射学及生物化学方面
Acta Paediatr Scand. 1978 Jan;67(1):113-9. doi: 10.1111/j.1651-2227.1978.tb16287.x.
9
[Indicative radiologic features in disseminated lipogranulomatosis (Farber's disease)].[播散性脂肪肉芽肿病（法伯病）的影像学特征]
Fortschr Geb Rontgenstr Nuklearmed. 1972 Jul;117(1):47-51.
10
[Farber's disease (disseminated lipogranulomatosis) (author's transl)].法伯氏病（播散性脂肪肉芽肿病）（作者译）
Monatsschr Kinderheilkd (1902). 1974 Apr;122(4):153-9.

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Acid Ceramidase Deficiency: Bridging Gaps between Clinical Presentation, Mouse Models, and Future Therapeutic Interventions.酸性 ceramidase 缺乏症：弥合临床表现、小鼠模型与未来治疗干预之间的差距。
Biomolecules. 2023 Feb 1;13(2):274. doi: 10.3390/biom13020274.
2
Acid Ceramidase Deficiency in Mice Results in a Broad Range of Central Nervous System Abnormalities.小鼠酸性神经酰胺酶缺乏导致广泛的中枢神经系统异常。
Am J Pathol. 2017 Apr;187(4):864-883. doi: 10.1016/j.ajpath.2016.12.005.
3
2'-hydroxy C16-ceramide induces apoptosis-associated proteomic changes in C6 glioma cells.

本文引用的文献

1
METHODS FOR METHANOLYSIS OF SPHINGOLIPIDS AND DIRECT DETERMINATION OF LONG-CHAIN BASES BY GAS CHROMATOGRAPHY.鞘脂类甲醇解及气相色谱法直接测定长链碱的方法
J Am Oil Chem Soc. 1965 Apr;42:294-8. doi: 10.1007/BF02540132.
2
Lipogranulomatosis; a new lipo-glycoprotein storage disease.脂肪肉芽肿病；一种新的脂肪糖蛋白贮积病。
J Mt Sinai Hosp N Y. 1957 Nov-Dec;24(6):816-37.
3
A simple method for the isolation and purification of total lipides from animal tissues.一种从动物组织中分离和纯化总脂质的简单方法。
2'-羟基 C16-神经酰胺诱导 C6 神经胶质瘤细胞凋亡相关的蛋白质组学变化。
J Proteome Res. 2013 Oct 4;12(10):4366-75. doi: 10.1021/pr4003432. Epub 2013 Sep 12.
4
Fatty acid 2-Hydroxylation in mammalian sphingolipid biology.哺乳动物鞘脂生物学中的脂肪酸2-羟基化作用
Biochim Biophys Acta. 2010 Apr;1801(4):405-14. doi: 10.1016/j.bbalip.2009.12.004. Epub 2009 Dec 21.
5
Substrate-specificities of acid and alkaline ceramidases in fibroblasts from patients with Farber disease and controls.法布里病患者和对照者成纤维细胞中酸性和碱性神经酰胺酶的底物特异性。
Biochem J. 1982 Aug 1;205(2):419-25. doi: 10.1042/bj2050419.
6
Farber's disease in two siblings, sural nerve and subcutaneous biopsies by light and electron microscopy.
Acta Neuropathol. 1986;72(2):178-88. doi: 10.1007/BF00685981.
7
Farber disease: an ultrastructural study. Report of a case and review of the literature.法伯病：超微结构研究。1例报告并文献复习。
Virchows Arch A Pathol Anat Histopathol. 1992;420(3):281-90. doi: 10.1007/BF01600282.
8
Ceramide metabolism in brain.大脑中的神经酰胺代谢
Mol Cell Biochem. 1979 Jan 15;23(1):17-25. doi: 10.1007/BF00226676.
J Biol Chem. 1957 May;226(1):497-509.
4
Enzymatic synthesis of ceramide.神经酰胺的酶促合成。
Biochim Biophys Acta. 1966 Dec 7;125(3):542-7. doi: 10.1016/0005-2760(66)90042-7.
5
Concentration and fatty acid composition of cerebrosides and sulfatides in mature and immature human brain.成熟和未成熟人脑中海藻糖脂和硫脂的浓度及脂肪酸组成
J Lipid Res. 1966 Jul;7(4):479-86.
6
Sulfatides of human kidney. Isolation, identification, and fatty acid composition.人肾硫脂。分离、鉴定及脂肪酸组成。
Biochim Biophys Acta. 1966 Jun 1;116(3):521-31. doi: 10.1016/0005-2760(66)90122-6.
7
Changes in sphingosine and fatty acid components of the gangliosides in developing rat and human brain.
J Lipid Res. 1966 Jan;7(1):122-31.
8
Fatty acid and fatty aldehyde composition of the major brain lipids in normal human gray matter, white matter, and myelin.正常人类灰质、白质和髓磷脂中主要脑脂质的脂肪酸和脂肪醛组成。
J Lipid Res. 1965 Oct;6(4):545-51.
9
[On the C18-and C20-sphingosine content of ceramides and sphingomyelins from the grey and white matter of the human brain].[关于人脑灰质和白质中神经酰胺和鞘磷脂的C18-和C20-鞘氨醇含量]
Hoppe Seylers Z Physiol Chem. 1969 Mar;350(3):373-8.
10
Changes in the fatty acid composition of cerebrosides and sulfatides of human nervous tissue with age.人类神经组织中脑苷脂和硫脂的脂肪酸组成随年龄的变化。
J Lipid Res. 1968 Mar;9(2):215-25.