Coto E O, Jimenez M Q, Castaneda A R, Rufilanchas J J, Deverall P B
Br Heart J. 1979 Jul;42(1):15-21. doi: 10.1136/hrt.42.1.15.
This series of 5 cases with double outlet of morphologically left ventricular chamber includes 4 found during a review of 1700 heart specimens (incidence 0.23%) and 1 found at operation and successfully corrected. Abnormal atrioventricular connection precluding total correction was present in the 4 anatomical cases. Clinical diagnosis may be difficult and it is suggested that axial cineangiography may make anatomical diagnosis easier. Absence of the infundibular septum and aortic laevoposition are frequent. As some cases can be surgically corrected, accurate information is required on the size of the right ventricle, the morphology and function of the atrioventricular valves, the presence, size, and position of the ventricular septal defect, and the degree and type of outflow tract obstruction.
这5例形态学上左心室双出口病例系列中,4例是在对1700份心脏标本进行回顾性研究时发现的(发病率为0.23%),1例是在手术中发现并成功矫正的。4例解剖学病例存在异常房室连接,无法进行完全矫正。临床诊断可能困难,有人提出轴位电影血管造影术可能使解剖学诊断更容易。漏斗间隔缺如和主动脉左位很常见。由于一些病例可以通过手术矫正,因此需要关于右心室大小、房室瓣形态和功能、室间隔缺损的存在、大小和位置以及流出道梗阻程度和类型的准确信息。