亨廷顿病和图雷特综合征。I. 床鬼的电子自旋共振
Huntington disease and Tourette syndrome. I. Electron spin resonance of bed ghosts.
作者信息
Comings D E, Pekkala A, Schuh J R, Kuo P C, Chan S I
出版信息
Am J Hum Genet. 1981 Mar;33(2):166-74.
Abstract
Abnormalities in the electron spin resonance (ESR) of nitroxide-labeled red blood cell membranes have been reported in Huntington disease (HD). Because of the importance of verifying a general membrane defect in this disease, we have examined 13 unmedicated HD patients of all grades of severity, with a duration of symptoms from 3 to 20 years and including juvenile and rigid cases. No significance differences in the ESR of controls, HD patients, and three Tourette syndrome patients were found.
摘要
有报道称，亨廷顿舞蹈症（HD）患者中，氮氧化物标记的红细胞膜的电子自旋共振（ESR）存在异常。鉴于验证该病普遍存在膜缺陷的重要性，我们检查了13名未接受药物治疗、症状严重程度各异、症状持续时间为3至20年的HD患者，其中包括青少年患者和僵直型患者。未发现对照组、HD患者以及三名图雷特综合症患者的ESR存在显著差异。
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