Hastings D E, Evans J A
J Hand Surg Am. 1978 Mar;3(2):179-83. doi: 10.1016/s0363-5023(78)80069-0.
Three patients with lupus erythematosus developed severe hand deformities which, over the course of a year, went on to fixed volar subluxation of the proximal phalanges with some ulnar drift. The flexion deformity at the metacarpophalangeal joints of nearly 90 degrees was not correctable passively, and the palmar skin became macerated. The articular cartilage of the metacarpal heads and proximal phalanges was well preserved and replacement arthroplasty was not justified. Contracture not only in the intrinsics but also in the long flexors was not relieved by operation on the soft tissues. A step-cut metacarpal shortening did correct the remaining intrinsic and long flexor contracture, corrected the volar dislocation, restored full metacarpophalangeal extension, and maintained a full range of flexion. Position of the bones was maintained by intramedullary Steinmann pins and crossed Kirschner wires and, in one patient, by a small screw. No recurrences developed in the follow up period of 18 to 96 months.
三名红斑狼疮患者出现了严重的手部畸形,在一年的时间里,发展为近端指骨固定性掌侧半脱位,并伴有一定程度的尺侧偏斜。掌指关节近90度的屈曲畸形无法被动矫正,手掌皮肤出现浸渍。掌骨头和近端指骨的关节软骨保存良好,因此没有必要进行置换关节成形术。不仅内在肌挛缩,而且长屈肌挛缩,通过软组织手术也无法缓解。阶梯状掌骨缩短术确实纠正了剩余的内在肌和长屈肌挛缩,矫正了掌侧脱位,恢复了掌指关节的完全伸展,并保持了充分的屈曲范围。通过髓内斯氏针和交叉克氏针固定骨骼位置,在一名患者中还使用了一枚小螺钉。在18至96个月的随访期内未出现复发。