MacCarty R L, LaRusso N F, Wiesner R H, Ludwig J
Radiology. 1983 Oct;149(1):39-44. doi: 10.1148/radiology.149.1.6412283.
Cholangiograms of 86 patients with primary sclerosing cholangitis (PSC) were compared with those of 82 patients with primary bile duct carcinoma and 16 with primary biliary cirrhosis. Multifocal strictures involving both intra- and extra-hepatic bile ducts were most common in PSC; they were diffusely distributed, short, and annular, alternating with normal or slightly dilated segments to produce a "beaded" appearance. Very short, band-like strictures occurred in 18 patients; 9 also had diverticulum-like out-pouchings. Fourteen patients had "diverticula" without band strictures. Both findings appear to be specific for PSC. Inflammatory bowel disease was seen in 57 patients (66%), who could not be distinguished cholangiographically from other PSC patients. Of 40 patients with adequate retrograde pancreatograms, 3 had abnormalities of the pancreatic ducts.
对86例原发性硬化性胆管炎（PSC）患者的胆管造影结果与82例原发性胆管癌患者及16例原发性胆汁性肝硬化患者的胆管造影结果进行了比较。多灶性狭窄累及肝内和肝外胆管在PSC中最为常见；这些狭窄呈弥漫性分布，短且呈环形，与正常或轻度扩张的节段交替出现，形成“串珠样”外观。18例患者出现非常短的带状狭窄；其中9例还伴有憩室样外突。14例患者有“憩室”但无带状狭窄。这两种表现似乎对PSC具有特异性。57例患者（66%）患有炎症性肠病，在胆管造影上无法将他们与其他PSC患者区分开来。在40例逆行胰管造影充分的患者中，3例胰管有异常。
