获得性低丙种球蛋白血症与结节病。
Acquired hypogammaglobulinaemia and sarcoidosis.
作者信息
Lee C A
出版信息
Postgrad Med J. 1984 Aug;60(706):551-3. doi: 10.1136/pgmj.60.706.551.
Abstract
A syndrome has been described in which hypogammaglobulinaemia is associated with splenomegaly and haemolytic anaemia and also non-caseating granulomata in lymph nodes, liver, spleen and skin. This report describes a patient with this syndrome who in addition had a positive Kveim and elevated serum angiotensin converting enzyme (SACE), suggesting the diagnosis of sarcoidosis.
摘要
已描述了一种综合征，其中低丙种球蛋白血症与脾肿大、溶血性贫血相关，且在淋巴结、肝脏、脾脏和皮肤中还存在非干酪样肉芽肿。本报告描述了一名患有该综合征的患者，该患者此外还有阳性的克维姆试验结果以及血清血管紧张素转换酶（SACE）升高，提示结节病的诊断。
相似文献
1
Acquired hypogammaglobulinaemia and sarcoidosis.获得性低丙种球蛋白血症与结节病。
Postgrad Med J. 1984 Aug;60(706):551-3. doi: 10.1136/pgmj.60.706.551.
2
[Sarcoidosis with hematologic involvement and hypogammaglobulinemia].
Arch Pediatr. 1996 Jun;3(6):576-9. doi: 10.1016/0929-693x(96)83231-3.
3
Sarcoidosis and primary hypogammaglobulinaemia: a report of two cases and a review of the literature.结节病与原发性低丙种球蛋白血症：两例报告及文献综述
Sarcoidosis. 1985 Sep;2(2):91-5.
4
Massive splenomegaly, pancytopenia and haemolytic anaemia in sarcoidosis.
Acta Haematol. 1975;53(4):230-40. doi: 10.1159/000208188.
5
Fatal haemolytic anaemia complicating a case of common variable hypogammaglobulinaemia.致命性溶血性贫血并发一例常见变异型低丙种球蛋白血症。
Scott Med J. 1990 Oct;35(5):147-8. doi: 10.1177/003693309003500509.
6
Serum angiotensin-converting enzyme estimation and the Kveim-Siltzbach test in sarcoidosis.结节病中血清血管紧张素转换酶测定及克维姆-席尔茨巴赫试验
S Afr Med J. 1982 Apr 24;61(17):620-1.
7
Fuchs' heterochromic uveitis and sarcoidosis.富克斯异色性葡萄膜炎和结节病。
Br J Ophthalmol. 1995 Nov;79(11):1021-3. doi: 10.1136/bjo.79.11.1021.
8
Letter: Thrombocytopenia, haemolytic anaemia, and sarcoidosis.信函：血小板减少症、溶血性贫血与结节病。
Br Med J. 1976 Jan 3;1(6000):44. doi: 10.1136/bmj.1.6000.44.
9
Thrombocytopenia, haemolytic anaemia, and sarcoidosis.血小板减少症、溶血性贫血和结节病。
Br Med J. 1975 Nov 22;4(5994):440-1. doi: 10.1136/bmj.4.5994.440-a.
10
A case of primary idiopathic hypogammaglobulinaemia associated with haemolytic anaemia.一例原发性特发性低丙种球蛋白血症合并溶血性贫血。
Postgrad Med J. 1962 May;38(439):292-5. doi: 10.1136/pgmj.38.439.292.
本文引用的文献
1
Agammaglobulinemia.无丙种球蛋白血症
Pediatrics. 1952 Jun;9(6):722-8.
2
Syndrome of hypogammaglobulinemia, splenomegaly and hypersplenism.低丙种球蛋白血症、脾肿大和脾功能亢进综合征。
Blood. 1957 Oct;12(10):926-32.
3
Acquired agammaglobulinemia: report of three cases.
J Am Med Assoc. 1954 Dec 11;156(15):1390-3. doi: 10.1001/jama.1954.02950150012003.
4
Agammaglobulinemia.无丙种球蛋白血症
Ann Intern Med. 1954 Sep;41(3):629-39. doi: 10.7326/0003-4819-41-3-629.
5
Pre-B cells; normal and abnormal development.前B细胞；正常与异常发育
J Clin Immunol. 1981 Apr;1(2):81-9. doi: 10.1007/BF00915383.
6
Transient antibody deficiency and abnormal T suppressor cells induced by phenytoin.苯妥英诱导的短暂性抗体缺乏和异常抑制性T细胞
N Engl J Med. 1982 Feb 18;306(7):406-9. doi: 10.1056/NEJM198202183060707.
7
The gamma globulins. 3. The antibody deficiency syndromes.γ球蛋白。3. 抗体缺陷综合征。
N Engl J Med. 1966 Sep 29;275(13):709-15 contd. doi: 10.1056/NEJM196609292751307.
8
Infectious agammaglobulinemia: transmission of immunodeficiency with grafts of agammaglobulinemic cells.传染性无丙种球蛋白血症：无丙种球蛋白血症细胞移植导致免疫缺陷的传播。
J Exp Med. 1974 Oct 1;140(4):1097-1101. doi: 10.1084/jem.140.4.1097.
9
Role of suppressor T cells in pathogenesis of common variable hypogammaglobulinaemia.抑制性T细胞在常见变异型低丙种球蛋白血症发病机制中的作用。
Lancet. 1974 Sep 14;2(7881):609-13. doi: 10.1016/s0140-6736(74)91940-0.
10
Sarcoidosis and selective IgA deficiency.结节病与选择性IgA缺乏症。
Br J Dis Chest. 1978 Apr;72(2):143-6. doi: 10.1016/0007-0971(78)90025-6.
Zotero 插件