Whittaker J S, Pickering C A, Heath D, Smith P
Diagn Histopathol. 1983 Apr-Jun;6(2):77-84.
A Cypriot male of 22 years died after suffering recurrent daily haemoptyses of varying severity and slowly increasing effort intolerance for a period of four and a half years. Examination of a lung biopsy specimen revealed dilated vascular channels suggestive of a congenital anomaly of the pulmonary vasculature. Histological examination of the lung following necropsy revealed the diagnosis of pulmonary capillary haemangiomatosis. In this condition sheets of thin-walled blood vessels infiltrate the lung parenchyma, the walls of pulmonary arteries and veins, the bronchi and the pleura. The infiltration of pulmonary veins and venules induces secondary pulmonary veno-occlusive disease. This appears to be the second example of this disease which has been reported. It is open to clinical and histological mis-diagnosis and clinicians and pathologists should be aware of the existence of this entity.
一名22岁的塞浦路斯男性，在经历了四年半时间里反复出现的、严重程度各异的每日咯血以及逐渐加重的劳力性不耐受后死亡。对一份肺活检标本的检查显示血管通道扩张，提示存在先天性肺血管异常。尸检后对肺部进行的组织学检查确诊为肺毛细血管瘤病。在这种疾病中，薄壁血管片浸润肺实质、肺动脉和静脉壁、支气管以及胸膜。肺静脉和小静脉的浸润引发继发性肺静脉闭塞性疾病。这似乎是已报道的该疾病的第二个病例。它容易在临床和组织学上被误诊，临床医生和病理学家应意识到这种疾病的存在。
