Wagenvoort C A, Beetstra A, Spijker J
Histopathology. 1978 Nov;2(6):401-6. doi: 10.1111/j.1365-2559.1978.tb01734.x.
A case of capillary haemangiomatosis affecting both lungs. The angiomatous growth involved particularly the intralobular fibrous septa and appeared locally aggressive as it had destroyed and obstructed the pulmonary veins and venules. Some pulmonary arteries and bronchi were affected to a lesser extent. Pulmonary venous obstruction, sometimes simulating pulmonary veno-occlusive disease, caused severe haemosiderosis and interstitial fibrosis. The clinical features and the lung biopsy erroneously suggested a diagnosis of primary pulmonary haemosiderosis. No comparable case has been found in the literature.
一例累及双肺的毛细血管瘤病。血管瘤样生长特别累及小叶内纤维间隔,表现出局部侵袭性,因为它破坏并阻塞了肺静脉和小静脉。一些肺动脉和支气管也有较轻程度的受累。肺静脉阻塞有时类似肺静脉闭塞性疾病,导致严重的含铁血黄素沉着症和间质纤维化。临床特征和肺活检错误地提示原发性肺含铁血黄素沉着症的诊断。文献中未发现类似病例。