Papale J J, Akiwama K, Hirose T, Tsubota K, Hanaoka K, Albert D M
Arch Ophthalmol. 1984 Jan;102(1):100-3. doi: 10.1001/archopht.1984.01040030084042.
Tumors arising from the pigment epithelium of the ciliary body are rare and most commonly occur in white adults. We describe a tumor that was clinically indistinguishable from a melanoma or medulloepithelioma occurring in a 7-year-old Japanese boy. Three months after initial evaluation, the eye was enucleated because of intractable intraocular pressure elevation and pain. On pathologic examination the tumor was found to fill approximately one third of the anterior chamber. Light microscopic and ultrastructural findings were consistent with an adenocarcinoma of the ciliary body pigment epithelium. To our knowledge, this is the youngest patient described with this tumor.
起源于睫状体色素上皮的肿瘤罕见，最常发生于成年白人。我们描述了一例临床上与黑色素瘤或髓上皮瘤难以区分的肿瘤，发生在一名7岁日本男孩身上。初次评估3个月后，因顽固性眼压升高和疼痛，该眼被摘除。病理检查发现肿瘤约占前房的三分之一。光镜和超微结构检查结果符合睫状体色素上皮腺癌。据我们所知，这是报道的患此肿瘤最年轻的患者。
