Capeder J, Müller W, Dalquen P, Campana A
Dtsch Med Wochenschr. 1982 Oct 29;107(43):1635-9. doi: 10.1055/s-2008-1070179.
Kartagener's syndrome (situs inversus totalis, bronchiectasis and sinusitis) was demonstrated in two patients. Electron microscopic investigations of the bronchial epithelium showed an accidental arrangement of ciliary axes, but not the expected lack of dynein arms. In both cases severe disturbance of maturation of spermiogenesis, not noted in this syndrome so far, was observed. Whereas one patient is largely free of symptoms after two operations, the other died after the second operation as a consequence of bronchopleural fistulation and bilateral pneumonic complications.
两名患者被诊断为卡塔格内综合征(全内脏转位、支气管扩张和鼻窦炎)。对支气管上皮的电子显微镜检查显示,纤毛轴排列异常,但未发现预期的动力蛋白臂缺失。在这两个病例中,均观察到精子发生成熟的严重紊乱,这在该综合征中迄今尚未见报道。其中一名患者在两次手术后基本无症状,而另一名患者在第二次手术后因支气管胸膜瘘和双侧肺部并发症死亡。