Pfab R, Carl P
Helv Chir Acta. 1981 Aug;48(3-4):295-300.
Polycystic disease of the kidneys was found in 80 patients, who were members of 18 families. The disease could be demonstrated in 62 of 65 tested persons of these families. By ultrasound examination cyst formations could be detected already in the age of 6 years. The most common complications were urinary tract infections (46%), hypertension (30%) and nephrolithiasis (29%). Cysts of liver and pancreas were observed in 30%, cerebral hemorrhage in 6%. The frequency of hypertension and urinary tract infections as well as the occurrence of uremia increased in the fifth decennium.
在80名患者中发现了多囊肾病，他们是18个家族的成员。在这些家族的65名受测者中，有62人被证实患有该病。通过超声检查，在6岁时就可以检测到囊肿形成。最常见的并发症是尿路感染（46%）、高血压（30%）和肾结石（29%）。30%的患者观察到肝脏和胰腺囊肿，6%的患者出现脑出血。高血压和尿路感染的发生率以及尿毒症的发生率在第五个十年中有所增加。
