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表现为严重帕金森症的假性甲状旁腺功能减退症。

Pseudohypoparathyroidism presenting as severe Parkinsonism.

作者信息

Pearson D W, Durward W F, Fogelman I, Boyle I T, Beastall G

出版信息

Postgrad Med J. 1981 Jul;57(669):445-7. doi: 10.1136/pgmj.57.669.445.

DOI:10.1136/pgmj.57.669.445
PMID:7312741
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2424956/
Abstract

A case of pseudohypoparathyroidism in a middle-aged female presenting with severe Parkinsonism is reported. Correction of serum calcium led to marked clinical improvement suggesting that symptoms and signs were exacerbated by hypocalcaemia and tetanic spasm. Calcification of the basal ganglia was not detected on skull X-ray but was revealed by computerized axial tomography.

摘要

报告了一例患有严重帕金森症的中年女性假性甲状旁腺功能减退症病例。血清钙的纠正导致了显著的临床改善,这表明症状和体征因低钙血症和手足搐搦而加重。颅骨X线检查未发现基底神经节钙化,但计算机断层扫描显示有钙化。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2ba5/2424956/a7b6333fad06/postmedj00223-0041-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2ba5/2424956/a7b6333fad06/postmedj00223-0041-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2ba5/2424956/a7b6333fad06/postmedj00223-0041-a.jpg

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本文引用的文献

1
Computer tomography in basal ganglia calcification.
Clin Radiol. 1980 Mar;31(2):167-8. doi: 10.1016/s0009-9260(80)80147-4.
2
Estimation of skeletal involvement in primary hyperparathyroidism. Use of 24-hour whole-body retention of technetium-99m diphosphonate.
Ann Intern Med. 1980 Jan;92(1):65-7. doi: 10.7326/0003-4819-92-1-65.
3
A simplified assessment of response to parathyroid hormone in hypoparathyroid patients.对甲状旁腺功能减退患者甲状旁腺激素反应的简化评估。
Lancet. 1976 Jan 10;1(7950):62-4. doi: 10.1016/s0140-6736(76)90152-5.
双侧纹状体-苍白球-齿状核钙化(法尔病):7例报告及文献复习
BMC Neurol. 2016 Sep 8;16(1):165. doi: 10.1186/s12883-016-0693-1.
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Prolonged spontaneous normocalcaemia in pseudohypoparathyroidism from resorption of soft tissue calcium deposits: a cautionary tale.软组织钙沉积吸收导致的假性甲状旁腺功能减退症患者出现长期自发性血钙正常:一则警示故事。
BMJ Case Rep. 2014 Jan 30;2014:bcr2013202729. doi: 10.1136/bcr-2013-202729.
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Prevalences of CT-detected calcification in the basal ganglia in idiopathic hypoparathyroidism and pseudohypoparathyroidism.特发性甲状旁腺功能减退症和假性甲状旁腺功能减退症中CT检测到的基底节钙化的患病率。
Neuroradiology. 1985;27(1):32-7. doi: 10.1007/BF00342514.