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一例类似缺氧后动作性肌阵挛的运动障碍型脑瘫病例。

A case of dyskinetic cerebral palsy resembling post-anoxic action myoclonus.

作者信息

Sugama S, Kusano K

机构信息

Department of Pediatrics, Tokyo Metropolitan Kita Medical Rehabilitation Center for the Handicapped, Japan.

出版信息

Brain Dev. 1995 May-Jun;17(3):210-2. doi: 10.1016/0387-7604(95)00030-f.

DOI:10.1016/0387-7604(95)00030-f
PMID:7573763
Abstract

Myoclonus after brain anoxia is more commonly observed in adults. Perinatal anoxia, however, on rare occasions causes myoclonus as the main neurologic abnormality. In this paper we described a case of cerebral palsy complicated by chorea and tremulous movements of the foot in which there were no risk factors except perinatal asphyxia. The patient had unique symptoms, action myoclonus associated with the movements of hyperkinésie volitionnelle. This case illustrated two points. One is that abnormal involuntary movements attributed to perinatal brain insults had changed as the brain matured. The other is that some movements were very similar to those of the post-anoxic action myoclonus, commonly seen in patients who sustain brain damage in adulthood.

摘要

脑缺氧后肌阵挛在成人中更为常见。然而,围产期缺氧在极少数情况下会导致肌阵挛成为主要的神经学异常。在本文中,我们描述了一例脑瘫合并足部舞蹈样动作和震颤的病例,除围产期窒息外无其他危险因素。该患者有独特的症状,即与随意性运动增多相关的动作性肌阵挛。这个病例说明了两点。一是归因于围产期脑损伤的异常不自主运动随着大脑成熟而发生了变化。另一点是,一些运动与成年期脑损伤患者常见的缺氧后动作性肌阵挛非常相似。

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A case of dyskinetic cerebral palsy resembling post-anoxic action myoclonus.一例类似缺氧后动作性肌阵挛的运动障碍型脑瘫病例。
Brain Dev. 1995 May-Jun;17(3):210-2. doi: 10.1016/0387-7604(95)00030-f.
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