Stöve J, Reichelt A
Orthopaedic Department, University Hospital Freiburg, Germany.
Arch Orthop Trauma Surg. 1995;114(4):207-10. doi: 10.1007/BF00444264.
We report a case of a 49-year-old white woman with Gorham-Stout syndrome. This very rare massive osteolysis occurred in the left pelvis and included the femur and the sacral bone. Histology study revealed typical ectatic vessels covered with endothelium. The therapy of choice in this region is radiotherapy with a dose of 40 Gy. However, in our case this therapy only led to short-term pain relief and cessation of the osteolysis. Stabilization with corticospongious bone did not seem to be effective against the progressing osteolysis.
我们报告一例49岁患有戈勒姆-斯托特综合征的白人女性病例。这种极为罕见的大块骨质溶解发生在左骨盆，累及股骨和骶骨。组织学研究显示典型的扩张血管内衬内皮细胞。该部位的首选治疗方法是40 Gy剂量的放射治疗。然而，在我们的病例中，这种治疗仅带来短期疼痛缓解和骨质溶解停止。用皮质松质骨进行固定似乎对进展性骨质溶解无效。
