Mitochondrial protein transport--a system in search of mutations.
作者信息
Fenton W A
出版信息
Am J Hum Genet. 1995 Aug;57(2):235-8.
Abstract
摘要
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本文引用的文献
1
Mitochondrial protein import: specific recognition and membrane translocation of preproteins.线粒体蛋白质输入：前体蛋白的特异性识别与膜易位
J Membr Biol. 1993 Sep;135(3):191-207. doi: 10.1007/BF00211091.
2
Mitochondrial molecular chaperones: their role in protein translocation.线粒体分子伴侣：它们在蛋白质转运中的作用。
Trends Biochem Sci. 1994 Feb;19(2):87-92. doi: 10.1016/0968-0004(94)90041-8.
3
The protein import machinery of the mitochondrial inner membrane.线粒体内膜的蛋白质导入机制。
Trends Biochem Sci. 1994 Sep;19(9):368-72. doi: 10.1016/0968-0004(94)90113-9.
4
The role of Hsp70 in conferring unidirectionality on protein translocation into mitochondria.热休克蛋白70（Hsp70）在赋予蛋白质向线粒体转运的单向性方面的作用。
Science. 1994 Nov 18;266(5188):1250-3. doi: 10.1126/science.7973708.
5
Mitochondrial Hsp70/MIM44 complex facilitates protein import.线粒体热休克蛋白70/线粒体导入调节因子44复合物促进蛋白质导入。
Nature. 1994 Oct 27;371(6500):768-74. doi: 10.1038/371768a0.
6
7
Targeting of pre-ornithine transcarbamylase to mitochondria: definition of critical regions and residues in the leader peptide.鸟氨酸转氨甲酰酶前体靶向线粒体：前导肽中关键区域和残基的定义
Cell. 1986 Feb 14;44(3):451-9. doi: 10.1016/0092-8674(86)90466-6.
8
Arginine in the leader peptide is required for both import and proteolytic cleavage of a mitochondrial precursor.前导肽中的精氨酸对于线粒体前体的导入和蛋白水解切割都是必需的。
Proc Natl Acad Sci U S A. 1985 Aug;82(15):4930-3. doi: 10.1073/pnas.82.15.4930.
9
Import of rat ornithine transcarbamylase precursor into mitochondria: two-step processing of the leader peptide.大鼠鸟氨酸转氨甲酰酶前体导入线粒体：前导肽的两步加工过程。
J Cell Biol. 1987 Dec;105(6 Pt 1):2631-9. doi: 10.1083/jcb.105.6.2631.
10
The ornithine transcarbamylase leader peptide directs mitochondrial import through both its midportion structure and net positive charge.鸟氨酸转氨甲酰酶前导肽通过其中间部分结构和净正电荷引导线粒体导入。
J Cell Biol. 1987 Aug;105(2):669-77. doi: 10.1083/jcb.105.2.669.
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