Aylward G W, Sullivan T J, Garner A, Moseley I, Wright J E
Moorfields Eye Hospital, London.
Br J Ophthalmol. 1995 Mar;79(3):246-9. doi: 10.1136/bjo.79.3.246.
Multifocal fibrosclerosis is a condition of unknown aetiology, characterised by fibrous lesions occurring at a variety of sites. Clinical variants include retroperitoneal fibrosis, Riedel's thyroiditis, sclerosing cholangitis, and mediastinal fibrosis. Orbital pseudotumour has been reported as a manifestation of this condition. Three patients with multifocal fibrosclerosis in whom orbital involvement was the dominant feature are described.
多灶性纤维硬化是一种病因不明的病症,其特征是在多个部位出现纤维性病变。临床变体包括腹膜后纤维化、Riedel甲状腺炎、硬化性胆管炎和纵隔纤维化。眼眶假瘤已被报道为这种病症的一种表现形式。本文描述了3例以眼眶受累为主要特征的多灶性纤维硬化患者。