Drachtman R A, Alter B P
Division of Pediatric Hematology/Oncology, University of Medicine and Dentistry, New Jersey-Robert Wood Johnson Medical School, New Brunswick, USA.
Dermatol Clin. 1995 Jan;13(1):33-9.
Dyskeratosis congenita is a rare genodermatosis. Malignant deterioration and hematologic complications are well-described features of this syndrome. Correct recognition is essential for proper management. A review of diagnostic considerations and treatment guidelines is presented.