Drachtman R A, Alter B P
Division of Pediatric Hematology/Oncology, University of Medicine and Dentistry, New Jersey-Robert Wood Johnson Medical School, New Brunswick, USA.
Dermatol Clin. 1995 Jan;13(1):33-9.
Dyskeratosis congenita is a rare genodermatosis. Malignant deterioration and hematologic complications are well-described features of this syndrome. Correct recognition is essential for proper management. A review of diagnostic considerations and treatment guidelines is presented.
先天性角化不良是一种罕见的遗传性皮肤病。恶性恶化和血液学并发症是该综合征的典型特征。正确识别对于恰当的管理至关重要。本文对诊断要点和治疗指南进行了综述。
