Falkenbach A, Lembcke B, Schneider M, Wigand R, Mulert-Ernst R, Caspary W
Johann Wolfgang Goethe-University Hospital, Frankfurt am Main, FRG.
Clin Rheumatol. 1994 Sep;13(3):513-7. doi: 10.1007/BF02242954.
We report about a 25-year-old female patient, who met all the criteria of adult-onset Still's disease except for the typical nonpruric rash. The disease exacerbated during pregnancy. Polyserositis was the predominant clinical manifestation. The histological examination of the bone marrow biopsy revealed changes similar to those seen in a myelodysplastic syndrome. The clinical condition improved after therapy with high-dose steroids and cyclophosphamide.
我们报告了一名25岁的女性患者,她除了没有典型的非瘙痒性皮疹外,符合成人斯蒂尔病的所有标准。该疾病在怀孕期间加重。多浆膜炎是主要的临床表现。骨髓活检的组织学检查显示出与骨髓增生异常综合征中所见相似的变化。在接受大剂量类固醇和环磷酰胺治疗后,临床状况有所改善。