Currarino G, Willis K W, Johnson A F, Miller W W
AJR Am J Roentgenol. 1976 Nov;127(5):775-9. doi: 10.2214/ajr.127.5.775.
Pulmonary telangiectasia is an uncommon developmental anomaly characterized by minute arteriovenous fistulae disseminated throughout both lungs. It should be suspected in patients with cyanosis and digital clubbing who do not have chronic lung disease or a cyanotic cardiac anomaly. The presence of telangiectases of skin or mucous membranes in the patient or members of his family is an important diagnostic clue. The chest film usually shows a coarse spidery appearance of the peripheral vascular markings in the lungs. More specific findings are obtained in the pulmonary angiogram where the normally invisible capillary phase is replaced by irregular vascular channels bridging the peripheral branches of pulmonary arteries and veins. The intrapulmonary right-to-left shunt may be confirmed by pulmonary scintigraphy using technetium-labeled albumin. Two cases are presented with a brief review of the literature.
肺毛细血管扩张症是一种罕见的发育异常，其特征为遍布双肺的微小动静脉瘘。对于无慢性肺部疾病或青紫型心脏异常但有发绀和杵状指的患者，应怀疑此病。患者本人或其家族成员皮肤或黏膜存在毛细血管扩张是重要的诊断线索。胸部X线片通常显示肺部外周血管纹理呈粗蜘蛛网状。在肺血管造影中可获得更具特异性的表现，正常情况下不可见的毛细血管期被连接肺动脉和肺静脉外周分支的不规则血管通道所取代。使用锝标记白蛋白的肺闪烁显像可证实肺内右向左分流。本文报告两例病例并简要回顾文献。
