Jacobs J P, Konstantakos A K, Holland F W, Herskowitz K, Ferrer P L, Perryman R A
Division of Thoracic and Cardiovascular Surgery, University of Miami/Jackson Memorial Medical Center, Florida.
Ann Thorac Surg. 1994 Nov;58(5):1552-5. doi: 10.1016/0003-4975(94)91963-1.
Cardiac rhabdomyomas are the most common cardiac tumor in children. These tumors may cause obstruction to blood flow, valvular insufficiency, and cardiac arrhythmias. We present two cases of cardiac rhabdomyomas in infants that were managed surgically and review the literature. Without surgical intervention, the prognosis for symptomatic cardiac rhabdomyomas is dismal, with eventual death likely due to heart failure or arrhythmias. As our two cases indicate, surgical treatment may improve this prognosis. Pediatric cardiac rhabdomyomas should be resected when the tumors cause hemodynamic compromise or cardiac arrhythmias.
心脏横纹肌瘤是儿童最常见的心脏肿瘤。这些肿瘤可能导致血流梗阻、瓣膜功能不全和心律失常。我们报告两例婴儿心脏横纹肌瘤经手术治疗的病例并复习相关文献。若不进行手术干预,有症状的心脏横纹肌瘤预后不佳,最终可能因心力衰竭或心律失常而死亡。正如我们的两例病例所示,手术治疗可能改善这种预后。当肿瘤导致血流动力学障碍或心律失常时,小儿心脏横纹肌瘤应予以切除。