Wells R G, Sty J R, Brummond R A
Department of Radiology, Children's Hospital of Wisconsin, Milwaukee 53226.
Wis Med J. 1994 Sep;93(9):467-8.
Hemolytic uremic syndrome is characterized by an abrupt onset of a microangiopathy, thrombocytopenia, hemolytic anemia and renal failure. These abnormalities present in varying degrees. The vascular abnormalities include endothelial swelling and thrombus formation. The kidney is the major target of involvement, although intestines, lung and brain may also be affected. It is considered a disease of the infant, although it occurs in older children and adults as a component of thrombotic thrombocytopenic purpura. We present the sonographic findings of adrenal involvement in a child with hemolytic uremic syndrome, which seems to be a rare occurrence. The patient developed adrenal insufficiency during the acute phase of the disease.
溶血性尿毒症综合征的特征是微血管病、血小板减少、溶血性贫血和肾衰竭突然发作。这些异常表现程度各异。血管异常包括内皮肿胀和血栓形成。肾脏是主要受累靶器官，不过肠道、肺和脑也可能受到影响。尽管它在大龄儿童和成人中作为血栓性血小板减少性紫癜的一部分出现，但它被认为是一种婴幼儿疾病。我们展示了一名溶血性尿毒症综合征患儿肾上腺受累的超声检查结果，这似乎很少见。该患者在疾病急性期出现了肾上腺功能不全。
