Ferrante A, Pedi C, Cusumano S, Malfitano D
Servizio di Cardiologia, Ospedale Gravina, Caltagirone.
G Ital Cardiol. 1994 Sep;24(9):1121-4.
We report a case of left pericardial agenesia in a 44 year old woman. Clinical picture was not specific on clinical field: atypical chest pain, asthenia, syncope, cystolic murmur 1/6 Levine on the second left interspace were found. ECG showed clockwise deviation of axis in the precordial leads and incomplete right bundle branch block. Chest X-ray showed marked levocardia and dilatation of pulmonary trunk. Levocardia increased with the patient on the left side. Echocardiography (possible only with patient recumbent on his right side) was normal. Magnetic resonance imaging showed absence of the left pericardium. We analyse the diagnostic problems and the prognostic doubts of this rare congenital anomaly.
我们报告一例44岁女性左心包缺如的病例。临床症状在临床领域无特异性：发现有非典型胸痛、乏力、晕厥，在左第二肋间可闻及1/6级莱文氏收缩期杂音。心电图显示胸前导联电轴顺时针偏移及不完全性右束支传导阻滞。胸部X线显示明显左位心及肺动脉干扩张。患者左侧卧位时左位心更明显。超声心动图（仅患者右侧卧位时可行）正常。磁共振成像显示左心包缺如。我们分析了这种罕见先天性异常的诊断问题及预后疑虑。
