Furie D M, Tien R D
Department of Radiology, Duke University Medical Center, Durham, NC 27710.
AJR Am J Roentgenol. 1994 May;162(5):1205-9. doi: 10.2214/ajr.162.5.8166011.
Cephalocervical fibromuscular dysplasia is an uncommon vascular disease that affects less than 1% of the population. Although often an incidental finding, patients may present with transient ischemic attacks, cerebral infarctions, or subarachnoid hemorrhage. Fibromuscular dysplasia is usually diagnosed in the fourth or fifth decade of life; it occurs in women more often than in men and in whites more frequently than in blacks. The purpose of this essay is to illustrate the broad spectrum of neuroimaging findings seen on CT scans, MR images, and angiograms of patients with cephalocervical fibromuscular dysplasia. The value of MR imaging in distinguishing tubular fibromuscular dysplasia from arterial dissection and arterial hypoplasia is demonstrated.
头颈部纤维肌发育不良是一种罕见的血管疾病，影响不到1%的人群。尽管通常是偶然发现，但患者可能会出现短暂性脑缺血发作、脑梗死或蛛网膜下腔出血。纤维肌发育不良通常在生命的第四个或第五个十年被诊断出来；女性比男性更易发生，白人比黑人更常见。本文的目的是说明头颈部纤维肌发育不良患者在CT扫描、磁共振成像（MR）和血管造影上所见的广泛神经影像学表现。证明了MR成像在区分管状纤维肌发育不良与动脉夹层和动脉发育不全方面的价值。
