Matamala Gimeno C, Pérez Calvo J I, Amores Ferreras M
Servicio de Medicina Interna B, Hospital Clínico Universitario, Zaragoza.
An Med Interna. 1994 Feb;11(2):95-9.
Multiple Symmetric Lipomatosis (MSL or Madelung's Disease) is a rare entity characterized by the presence of non-capsulated lipomas mainly located at the neck and upper part of the thorax and frequently associated to chronic hepatopathy, neuropathy and alcoholic habit. We review and update the clinical, etiopathogenic, diagnostic and therapeutical aspects of this rare entity. We stress the presence of neuropathy, a typical feature of the disease, which has also a predictive value.
多发性对称性脂肪瘤病(MSL或马德隆氏病)是一种罕见的疾病,其特征是存在主要位于颈部和胸部上部的无包膜脂肪瘤,且常与慢性肝病、神经病变和酗酒习惯相关。我们回顾并更新了这种罕见疾病的临床、病因、诊断和治疗方面的内容。我们强调神经病变的存在,这是该疾病的一个典型特征,也具有预测价值。