Sepúlveda W H, Quiroz V H, Giuliano A, Henríquez R
Department of Obstetrics and Gynecology, Guillermo Grant Benavente Hospital, Concepción, Chile.
J Perinat Med. 1993;21(3):241-6. doi: 10.1515/jpme.1993.21.3.241.
Acardiac twinning is a rare complication of monozygotic twin gestation occurring in 1/35,000 pregnancies or in 1% of all monozygotic twins. This condition is characterized by partial or complete lack of development of the heart in one of the twins, and requires that the normal twin (pump twin) provides circulation for itself as well as the acardiac sibling (perfused twin) by means of reverse circulation through large artery-to-artery and vein-to-vein anastomoses. The acardiac anomaly is uniformly fatal for the perfused twin, and the perinatal mortality for the normal twin is about 50%, usually as the result of congestive heart failure, polyhydramnios, and preterm delivery. In this report we present two cases of acardiac twin prenatally diagnosed by ultrasound. The principal sonographic features for prenatal diagnosis and the clinical management are briefly discussed.
无心畸形是单卵双胎妊娠的一种罕见并发症，发生率为1/35000次妊娠，或占所有单卵双胎的1%。这种情况的特征是其中一个胎儿心脏部分或完全发育不全，正常胎儿（供血胎儿）需要通过大动脉与大动脉、静脉与静脉的吻合支进行逆向循环，为自身以及无心畸形的同胞胎儿（受血胎儿）提供血液循环。无心畸形对受血胎儿必然是致命的，正常胎儿的围产期死亡率约为50%，通常是由于充血性心力衰竭、羊水过多和早产所致。在本报告中，我们介绍了两例经超声产前诊断为无心畸形双胎的病例。简要讨论了产前诊断的主要超声特征及临床处理方法。
