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[婴儿颈部纵隔神经母细胞瘤手术经验]

[Experience with a operated cervico-mediastinal neuroblastoma in infant].

作者信息

Kunihara T, Matano J, Myojin K, Takeda T

机构信息

Department of Cardiovascular Surgery, National Sapporo Hospital, Japan.

出版信息

Kyobu Geka. 1994 Feb;47(2):160-3.

PMID:8301910
Abstract

Cervical neuroblastoma is relatively rare and shows very good prognosis. We reported a case of surgically resected cervico-mediastinal neuroblastoma. A 7-month-old boy was pointed out to have Horner syndrome (right ptosis and anhidrosis) and an abnormal shadow at right cervico-mediastinum on chest X-ray film during his stay in another hospital because of acute bronchitis. On examination after admission in our hospital, 3 x 4 cm size mass was palpated at the right neck and urine VMA and HVA level were elevated. The close examination demonstrated no sign of tumor in any other organ and tissue, which suggested that the tumor was cervical origin. 9 x 5, 5 x 3 cm tumor was almost removed and patient received chemotherapy. He is now free from disease at 1 year after operation.

摘要

颈部神经母细胞瘤相对罕见,预后非常好。我们报告了一例经手术切除的颈纵隔神经母细胞瘤病例。一名7个月大的男孩因急性支气管炎在另一家医院住院期间,胸部X线片显示有霍纳综合征(右侧上睑下垂和无汗)以及右颈纵隔异常阴影。我院入院检查时,在右侧颈部可触及一个3×4厘米大小的肿块,尿香草扁桃酸(VMA)和高香草酸(HVA)水平升高。进一步检查未发现其他任何器官和组织有肿瘤迹象,提示肿瘤起源于颈部。9×5、5×3厘米大小的肿瘤几乎被切除,患者接受了化疗。术后1年,他目前无病生存。

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1
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Kyobu Geka. 1994 Feb;47(2):160-3.
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Superior mediastinal syndrome with Rowland-Payne syndrome: an unusual presentation of cervico-mediastinal neuroblastoma.伴有罗兰-佩恩综合征的上纵隔综合征:一种颈纵隔神经母细胞瘤的罕见表现。
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Congenital Horner's syndrome associated with cervical neuroblastoma.先天性霍纳综合征合并颈部神经母细胞瘤。
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