Ochonisky S, Intrator L, Wechsler J, Revuz J, Bagot M
Service de Dermatologie, Hôpital Henri-Mondor, Créteil, France.
Dermatology. 1993;186(4):261-3. doi: 10.1159/000247366.
We report the case of a previously healthy 54-year-old woman, without any family history, who developed an angioneurotic edema with acquired C1 inhibitor deficiency and systemic lupus erythematosus. The search for a lymphoproliferative disorder was negative. Hydroxychloroquine therapy induced simultaneous resolution of lupus and angioedema. The pathophysiology of this association is discussed.
我们报告了一例既往健康、无家族病史的54岁女性病例，该患者出现了伴有获得性C1抑制物缺乏的血管性水肿和系统性红斑狼疮。对淋巴增殖性疾病的检查结果为阴性。羟氯喹治疗使狼疮和血管性水肿同时得到缓解。本文讨论了这种关联的病理生理学。
