Bertão Maria I, Fontaínhas Sara, Santos Silva Rosário, Ramalho Pedro, Gonçalves Abílio
Internal Medicine, Hospital Distrital Figueira da Foz, Figueira da Foz, PRT.
Pulmonology, Hospital Distrital Figueira da Foz, Figueira da Foz, PRT.
Cureus. 2024 Dec 19;16(12):e76023. doi: 10.7759/cureus.76023. eCollection 2024 Dec.
Cystic cuboid adenomatous malformations (CCAM) are congenital pulmonary lesions, usually benign, that can progress into malignancy. Bronchopulmonary sequestration (BPS) is another type of malformation that consistsof an ectopic pulmonary tissue mass that doesn't participate in blood-gas exchanges, with vascularization provided by anomalous branches of the thoracic aorta. Hybrid lesions are lesions that have histological features of CCAM but with systemic vascularization, a pathognomonic sign of BPS. These lesions are rare and difficult to diagnose. The diagnoses are mostly made in the pre-or neonatal phases of life. The diagnosis in adults is uncommon. The treatment is surgical resection of the lesion or wedge lobectomy. The case report describes a case of a hybrid lesion diagnosed in an asymptomatic adult, as well as a review of the adequate diagnostic workup for pulmonary lesions. In the literature, there are few cases of congenital lung lesions described in adults.
囊性长方体腺瘤样畸形（CCAM）是先天性肺部病变，通常为良性，但可发展为恶性。支气管肺隔离症（BPS）是另一种畸形，由不参与血气交换的异位肺组织块组成，其血管供应来自胸主动脉的异常分支。混合性病变是指具有CCAM组织学特征但伴有体循环血管化的病变，这是BPS的特征性表现。这些病变罕见且难以诊断。诊断大多在生命的产前或新生儿期做出。成人诊断并不常见。治疗方法是手术切除病变或楔形肺叶切除术。该病例报告描述了一例在无症状成人中诊断出的混合性病变病例，以及对肺部病变进行充分诊断检查的综述。在文献中，成人先天性肺部病变的病例很少被描述。
