Fékété F, Noun R, Sauvanet A, Fléjou J F, Bernades P, Belghiti J
Department of Digestive Surgery, University of Paris VII-Faculté Xavier Bichat, Beaujon Hospital, Clichy-Paris, France.
World J Surg. 1996 Mar-Apr;20(3):295-8. doi: 10.1007/s002689900047.
Cystic dystrophy in heterotopic pancreas (CDHP) is characterized by the presence of cystic formations surrounded by inflammation and scarring. It usually involves the duodenal wall and can be responsible for strictures and pain. The diagnosis of this disorder was previously based on pancreatoduodenectomy specimens removed for a suspected pancreatic tumor. Six cases were observed in young men (mean age 40 years) between 1989 and 1993. Computed tomography (CT) and endoscopic ultrasonography (EUS) features allowed definitive preoperative diagnosis of CDHP. After surgical resection of the tissue-bearing segments that included five pancreatoduodenectomies and one antrectomy, symptoms disappeared in all patients. Patients were followed 2 to 45 months; one patient experienced recurrence of pain and hyperamylasemia 17 months after surgery. The preoperative diagnosis of CDHP is presently possible because of modern imaging procedures and improved knowledge of specific signs. Resection is the most appropriate treatment.
异位胰腺的囊性营养不良（CDHP）的特征是存在被炎症和瘢痕组织包围的囊性结构。它通常累及十二指肠壁，可导致狭窄和疼痛。此前，这种疾病的诊断基于因疑似胰腺肿瘤而切除的胰十二指肠切除术标本。1989年至1993年间，在年轻男性（平均年龄40岁）中观察到6例。计算机断层扫描（CT）和内镜超声检查（EUS）特征有助于术前明确诊断CDHP。在对包括5例胰十二指肠切除术和1例胃窦切除术在内的含组织节段进行手术切除后，所有患者的症状均消失。对患者进行了2至45个月的随访；1例患者在术后17个月出现疼痛复发和高淀粉酶血症。由于现代成像技术和对特定体征认识的提高，目前已能够对CDHP进行术前诊断。手术切除是最合适的治疗方法。
