Barrall J L, Summers C G
Department of Ophthalmology, University of Minnesota, Minneapolis, USA.
Surv Ophthalmol. 1996 May-Jun;40(6):500-4. doi: 10.1016/s0039-6257(96)82016-9.
Ocular ischemic syndrome is extremely rare in childhood. Patients with moyamoya disease may be particularly susceptible to the development of ocular ischemia due to the associated carotid occlusion. A 19-month-old boy presented with neurofibromatosis and signs of ocular ischemia. At 29 months of age, he developed dense right vitreous hemorrhage and eventually lost vision in that eye due to phthisis. At almost six years of age, he developed an acute hemiplegia and was then diagnosed with moyamoya disease. This rare instance of childhood ocular ischemia in conjunction with moyamoya disease and neurofibromatosis demonstrates the serious ocular and systemic sequelae of occlusive vascular disease.
眼部缺血综合征在儿童期极为罕见。烟雾病患者可能因相关的颈动脉闭塞而特别容易发生眼部缺血。一名19个月大的男孩患有神经纤维瘤病并出现眼部缺血症状。在29个月大时，他出现了严重的右眼玻璃体积血，最终因眼球痨而失去了那只眼睛的视力。在将近六岁时，他出现了急性偏瘫，随后被诊断为烟雾病。这种儿童期眼部缺血与烟雾病和神经纤维瘤病并发的罕见病例表明了闭塞性血管疾病严重的眼部和全身后遗症。
