Fabre M, Terrier-Lacombe M J
Service d'Anatomie et de Cytologie Pathologiques, CHU Bicêtre, Le Kremlin-Bicêtre.
Arch Anat Cytol Pathol. 1996;44(1):49-52.
Rhabdoid tumour of the kidney is a rare, distinct clinico-pathological entity, mostly occurring in children, with an extremely aggressive behaviour. There is a wide range of histologic patterns. We report a case in which the classical "rhabdoid" cytology with eosinophilic cytoplasmic inclusions and macronucleoli was scanty and abundant cytoplasm was absent. Immunocytochemical and ultrastructural studies were essential. This poorly differentiated type of rhabdoid tumour must not be confused with Wilms' tumour because it requires an intensive chemotherapy regimen.
肾横纹肌样瘤是一种罕见的、独特的临床病理实体，主要发生于儿童，具有极强的侵袭性。其组织学模式多种多样。我们报告了一例病例，其中具有嗜酸性细胞质包涵体和大核仁的典型“横纹肌样”细胞学特征很少见，且缺乏丰富的细胞质。免疫细胞化学和超微结构研究至关重要。这种低分化型横纹肌样瘤绝不能与肾母细胞瘤混淆，因为它需要强化化疗方案。
