Irvine A D, Sweeney L, Corbett J R
Department of Dermatology, Royal Belfast Hospital for Sick Children, Northern Ireland.
Br J Dermatol. 1996 Jun;134(6):1135-7.
A boy with long-standing congenital cutaneous lymphangioma circumscriptum (LC), presented at the age of 6 years with an episode of painless haematuria, subsequently attributed to bladder wall involvement of a paravesical cystic retroperitoneal lymphangioma. Magnetic resonance imaging demonstrated this lymphangioma to be in communication with the cutaneous lesions. Deep lymphatic and visceral involvement is an extremely unusual occurrence in association with LC. This is the first report of an association between LC and cystic retroperitoneal lymphangioma. LC occasionally heralds a deeper, more clinically significant lymphangioma which may not become apparent until many years after the initial dermatological presentation. We report this case to raise awareness of this potential association and to demonstrate the usefulness of magnetic resonance imaging in the assessment of the deep component of cutaneous lymphangiomas.
一名患有长期先天性局限性皮肤淋巴管瘤（LC）的男孩，6岁时出现无痛性血尿，随后发现是膀胱壁受膀胱旁囊性腹膜后淋巴管瘤累及所致。磁共振成像显示该淋巴管瘤与皮肤病变相通。LC合并深部淋巴管和内脏受累极为罕见。这是首例关于LC与囊性腹膜后淋巴管瘤关联的报告。LC偶尔预示着存在更深层、临床意义更大的淋巴管瘤，可能在最初皮肤表现出现多年后才显现。我们报告此病例以提高对这种潜在关联的认识，并展示磁共振成像在评估皮肤淋巴管瘤深部成分中的作用。
