Atalay S, Imamoglu A, Gümüs H, Gürdal M, Ozenci M
Department of Pediatric Cardiology, Ankara University, Turkey.
Pediatr Cardiol. 1996 Jan-Feb;17(1):40-2. doi: 10.1007/BF02505810.
A 9-year-old girl was admitted because she had had palpitations for 2 years. Her electrocardiogram revealed multifocal ectopic beats with left bundle branch morphology, sinoatrial block, and first- and second-degree atrioventricular blocks. Cross-sectional echocardiography demonstrated an enlarged left ventricle and filling defects and sacculations of the posterior left ventricular wall, apex, and septum. The diagnosis of arrhythmogenic right ventricular dysplasia (ARVD) was confirmed by endomyocardial biopsy and thallium 201 scintigraphy. We present this case because of the rarity of left ventricular involvement associated with ARVD. We also emphasize the value of echocardiography in the early diagnosis of ARVD.
一名9岁女孩因心悸2年入院。她的心电图显示多灶性异位搏动，呈左束支形态，存在窦房阻滞以及一度和二度房室阻滞。心脏超声心动图显示左心室增大，左心室后壁、心尖和室间隔有充盈缺损及囊状改变。心内膜心肌活检和铊201闪烁扫描证实了致心律失常性右心室发育不良（ARVD）的诊断。我们报告此病例是因为ARVD合并左心室受累较为罕见。我们还强调了超声心动图在ARVD早期诊断中的价值。
