Calabrese P R, Frank H D, Taubin H L
Cancer. 1977 Aug;40(2):895-7. doi: 10.1002/1097-0142(197708)40:2<895::aid-cncr2820400245>3.0.co;2-8.
Lymphangiomyomyoma is a tumor of lymphatic channels and lymph nodes, clinically manifested by recurrent chylous pleural effusions and ascites. The disease is usually progressive and unresponsive to surgery, chemotherapy, or irradiation. A case of lymphangiomyomatosis in a 24-year-old woman who presented with chylous ascites is described. The patient was treated with dietary fat restriction supplemented with medium chain triglycerides and has remained free of recurrent effusions for 2 years.
淋巴管平滑肌瘤是一种淋巴管和淋巴结的肿瘤，临床表现为反复出现乳糜性胸腔积液和腹水。该疾病通常呈进行性发展，对手术、化疗或放疗均无反应。本文描述了一名24岁女性淋巴管平滑肌瘤病患者，该患者表现为乳糜性腹水。患者接受了饮食脂肪限制并补充中链甘油三酯的治疗，至今已2年未再出现反复积液。
