Uroz Tristán J, García Urgellés X, Melián Pérez-Marín S
Servicio de Cirugía Pediátrica, Hospital Materno-Infantil, Las Palmas de Gran Canaria.
Cir Pediatr. 1996 Jan;9(1):40-1.
The Rapunzel Syndrome is a rare form of gastric trichobezoar extending throughout the bowel. A 8-year-old girl was admitted to our institution with a six months history of vomiting and astenia. Upper gastrointestinal contrast study showed a lot of filling defects in stomach and the first bowel loops. At laparotomy a large intraluminal mass is observed. Gastrotomy revealed a large tricobezoar with intestinal extension to jejunum, that were extracted. In rare instances, this syndrome presents with a confusing clinical picture. A detailed medical history is an essential point in the diagnosis.
长发公主综合征是一种罕见的胃毛石症,可延伸至整个肠道。一名8岁女孩因呕吐和乏力6个月病史入住我院。上消化道造影显示胃和近端肠袢有许多充盈缺损。剖腹探查时观察到一个大的腔内肿物。胃切开术发现一个大的毛石症,其肠道延伸至空肠,遂将其取出。在罕见情况下,该综合征会呈现出令人困惑的临床表现。详细的病史是诊断的关键要点。