Hand anomalies in Crouzon syndrome.

OBJECTIVE

To review the hand radiographs of patients with Crouzon syndrome, to look for extracranial manifestations of the condition at this site.

DESIGN

The hand radiographs of those with Crouzon syndrome attending the Craniofacial Service at Great Ormond Street between 1985 and 1996 were reviewed.

RESULTS

Thirty-three patients underwent a total of 34 radiographs, one patient having had a serial study. This revealed a range of minor anomalies. Most striking was the presence of carpal fusions in four cases, a feature which has not previously been reported.

CONCLUSION

The hands of Crouzon syndrome may have anomalies including carpal fusions, and these results are evidence that the condition may produce subtle effects on the hands.