一名6岁儿童的多中心性网状组织细胞增生症病例。

A case of multicentric reticulohistiocytosis in a 6-year-old child.

作者信息

Candell Chalom E, Elenitsas R, Rosenstein E D, Kramer N

机构信息

Department of Pediatrics, Arthritis and Rheumatic Disease Center, St. Barnabas Medical Center, Livingston, NJ, USA.

出版信息

J Rheumatol. 1998 Apr;25(4):794-7.

PMID:9558188

Abstract

Multicentric reticulohistiocytosis (MR) is a rare disease in which an infiltration of histiocytic cells causes destructive polyarthritis and characteristic cutaneous lesions. It predominantly affects women between the ages of 40 and 50 years. Effective treatment has not been well established. We describe a case diagnosed in a 6-year-old girl. This is the youngest patient with MR reported to date.

摘要

多中心网状组织细胞增多症（MR）是一种罕见疾病，其中组织细胞浸润会导致破坏性多关节炎和特征性皮肤病变。它主要影响40至50岁的女性。尚未确立有效的治疗方法。我们描述了一例在一名6岁女孩中诊断出的病例。这是迄今为止报道的最年轻的MR患者。