Brito J C, Holanda M M, Holanda G, da Silva J A
Serviçio de Neurologia e Neurocirirgua do Hospital Santa Isabel, João, Pessoa Paraĩba, Brasil.
Arq Neuropsiquiatr. 1997 Sep;55(3A):472-7. doi: 10.1590/s0004-282x1997000300020.
The authors report two cases of progressive facial hemiatrophy (PFH) associated with cranial nerves hyperexcitability. One of them (Case 1), a 41-year-old-woman noticed a slight atrophy on the left side of her face at age of ten. For the last three months, she has been suffering from fits of neuralgic pains on the left side of her face which have not ceased by drug treatment In view of this, a surgery procedure was planned for the patient. The other patient (Case 2), a 33-year-old-woman has a 8 year history which started with cutaneous abnormalities (white and dark spots). Two years later she observed that her right cheek and right thigh had got a mild atrophy. Frequently, she has been complaining of cramps in the mandibular region which are precipitated, sometimes, by opening the mouth. A probable relation between neural excitability and PHF is discussed.
作者报告了两例与颅神经兴奋性过高相关的进行性面部半侧萎缩(PFH)病例。其中一例(病例1),一名41岁女性在10岁时注意到左侧面部轻微萎缩。在过去三个月里,她一直遭受左侧面部神经痛发作,药物治疗未能使其停止。鉴于此,为该患者计划了手术程序。另一例患者(病例2),一名33岁女性有8年病史,始于皮肤异常(白色和深色斑点)。两年后,她发现右脸颊和右大腿出现轻度萎缩。她经常抱怨下颌区域痉挛,有时张嘴会诱发。文中讨论了神经兴奋性与PFH之间可能的关系。