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Dysregulation of the mitochondrial ATP-synthase in respiratory chain defects: first experience.

作者信息

Das A M, Ullrich K

机构信息

Department of Paediatrics, University of Hamburg, Eppendorf, Germany.

出版信息

J Inherit Metab Dis. 1998 Jun;21(3):220-3. doi: 10.1023/a:1005395417041.

DOI:10.1023/a:1005395417041
PMID:9686361
Abstract
摘要

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Dysregulation of the mitochondrial ATP-synthase in respiratory chain defects: first experience.
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本文引用的文献

1
Regulation of the mitochondrial ATP-synthase in skeletal muscle from children--a new diagnostic tool.
J Inherit Metab Dis. 1996;19(2):137-9. doi: 10.1007/BF01799413.
2
Regulation of the mitochondrial ATP-synthase in human fibroblasts.人成纤维细胞中线粒体ATP合酶的调控
Clin Chim Acta. 1994 Nov;231(1):61-8. doi: 10.1016/0009-8981(94)90254-2.
3
Human mitochondrial electron transport chain: assay of succinate: cytochrome c reductase in leukocytes, platelets and cultured fibroblasts.人类线粒体电子传递链：白细胞、血小板和培养的成纤维细胞中琥珀酸：细胞色素c还原酶的测定
Biochem Med. 1981 Apr;25(2):234-8. doi: 10.1016/0006-2944(81)90080-6.
4
The calcium-binding ATPase inhibitor protein from bovine heart mitochondria. Purification and properties.
J Biol Chem. 1988 Aug 15;263(23):11498-503.
5
Estimation of NADH oxidation in human skeletal muscle mitochondria.人体骨骼肌线粒体中NADH氧化的估计
Clin Chim Acta. 1986 Mar 28;155(3):263-73. doi: 10.1016/0009-8981(86)90246-9.
6
The binding and release of the inhibitor protein are governed independently by ATP and membrane potential in ox-heart submitochondrial vesicles.在牛心亚线粒体小泡中，抑制蛋白的结合与释放分别由ATP和膜电位独立调控。
Biochim Biophys Acta. 1988 Mar 30;933(1):12-21. doi: 10.1016/0005-2728(88)90051-5.
7
Regulation of the mitochondrial ATP synthase in intact rat cardiomyocytes.完整大鼠心肌细胞中线粒体ATP合酶的调控
Biochem J. 1990 Mar 1;266(2):355-61. doi: 10.1042/bj2660355.
8
The ATPase inhibitor protein in oxidative phosphorylation. The rate-limiting factor to phosphorylation in submitochondrial particles.氧化磷酸化中的ATP酶抑制蛋白。亚线粒体颗粒中磷酸化的限速因子。
Biochim Biophys Acta. 1979 Oct 10;548(1):72-84. doi: 10.1016/0005-2728(79)90188-9.