Berger A, Roger V, Wind P, Chevallier J M, Cugnenc P H
Service de Chirurgie Digestive, Hôpital Laennec, Paris.
J Chir (Paris). 1997 Dec;134(7-8):305-10.
Congenital dilatation of the bile duct is an uncommon lesion requiring surgical treatment. Complete excision of the diseased bile duct prevents development of carcinoma of the bile duct. We report three cases of congenital dilatation of the biliary three, each illustrating a particular aspect of the therapeutic strategy. One patient had an unusual anomaly of the pancreaticobiliary junction that required pancreaticoduodenectomy. Another patient developed carcinoma of the bile duct 15 years after an internal derivation of a choledochal cyst. The last patient had dilatations of the common and intrahepatic bile ducts associated with congenital hepatic fibrosis.
先天性胆管扩张是一种需要手术治疗的罕见病变。病变胆管的完全切除可预防胆管癌的发生。我们报告了三例先天性胆管扩张病例，每例都说明了治疗策略的一个特定方面。一名患者存在胰胆管交界处的异常畸形，需要进行胰十二指肠切除术。另一名患者在胆总管囊肿内引流术后15年发生了胆管癌。最后一名患者的肝外胆管和肝内胆管扩张与先天性肝纤维化相关。
