Ibrahim A E, Myles L, Lang D A, Ellison D W
Department of Histopathology, Southampton University Hospitals, NHS Trust, UK.
Brain Pathol. 1998 Oct;8(4):817-8.
We report the case of a boy aged 2 years with spina bifida and a lipomyelomeningocele which contained ectopic immature renal tissue. He presented with a swelling over the lumbosacral region, incontinence, and bilateral leg weakness. Histopathologic examination revealed adipose tissue in which a focus of fibrous tissue contained neuroglial elements, striated muscle fibres and clusters of glomeruloid structures surrounded by immature tubules. The differential diagnosis of teratoma and lipomyelomeningocele with nephrogenic rests is discussed with reference to possible pathogenesis.
我们报告了一名2岁患有脊柱裂和脂肪瘤型脊髓脊膜膨出的男孩病例，该膨出包含异位未成熟肾组织。他表现为腰骶部肿胀、大小便失禁和双侧腿部无力。组织病理学检查显示脂肪组织中一个纤维组织灶含有神经胶质成分、横纹肌纤维以及由未成熟肾小管围绕的肾小球样结构簇。参考可能的发病机制，讨论了畸胎瘤与伴有肾源性残留的脂肪瘤型脊髓脊膜膨出的鉴别诊断。
