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一名慢性淋巴细胞白血病患者的猝死

Sudden death in a patient with chronic lymphocytic leukemia.

作者信息

Beaubien E R, Wilson T W, Satkunam N

机构信息

Department of Medicine, University of Saskatchewan, Saskatoon.

出版信息

CMAJ. 1998 Nov 3;159(9):1123-5.

PMID:9835882
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1229781/
Abstract

The authors describe a 51-year-old man with chronic lymphocytic leukemia who presented with respiratory distress and then died suddenly while in hospital. Autopsy revealed pulmonary leukostasis and a large intracardiac mass containing mostly mature lymphocytes and fibrin. Although leukostasis and lymphocyte thrombi have been described (albeit rarely) in chronic lymphocytic leukemia, an intracardiac "clot" has not. It seems plausible that this intracardiac mass caused the patient's death.

摘要

作者描述了一名51岁的慢性淋巴细胞白血病男性患者,该患者出现呼吸窘迫,随后在医院突然死亡。尸检发现肺部白细胞淤滞以及一个大的心脏内肿物,其主要由成熟淋巴细胞和纤维蛋白组成。虽然在慢性淋巴细胞白血病中已描述过白细胞淤滞和淋巴细胞血栓形成(尽管很少见),但心脏内“血栓”尚未见报道。这个心脏内肿物导致患者死亡似乎是合理的。

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引用本文的文献

1
Sudden death due to leukostasis in a subject with undiagnosed chronic lymphocytic leukemia.患者患有未确诊的慢性淋巴细胞白血病,因白细胞淤滞而突然死亡。
Forensic Sci Med Pathol. 2021 Dec;17(4):693-699. doi: 10.1007/s12024-021-00406-9. Epub 2021 Aug 20.
2
Leukostasis in Chronic Lymphocytic Leukemia.慢性淋巴细胞白血病中的白细胞淤滞。
Am J Case Rep. 2020 Jul 3;21:e924798. doi: 10.12659/AJCR.924798.

本文引用的文献

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Acute cardiorespiratory failure as presenting symptom of chronic lymphocytic leukemia.
Neth J Med. 1996 Jul;49(1):33-7. doi: 10.1016/0300-2977(96)00008-3.
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Chronic lymphocytic leukemia.慢性淋巴细胞白血病
Cancer Treat Rev. 1996 Jan;22(1):1-13. doi: 10.1016/s0305-7372(96)90013-4.
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Intravascular leukocyte thrombi and aggregates as a cause of morbidity and mortality in leukemia.血管内白细胞血栓和聚集体是白血病发病和死亡的一个原因。
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J Clin Invest. 1973 Feb;52(2):350-8. doi: 10.1172/JCI107191.
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Blut. 1988 Jan;56(1):39-44. doi: 10.1007/BF00321058.
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[Therapeutic leukapheresis in a leukostasis syndrome complicating chronic lymphoid leukemia].[治疗慢性淋巴细胞白血病并发白细胞淤滞综合征的白细胞去除术]
Ann Med Interne (Paris). 1988;139 Suppl 1:53-4.