Matsuo K, Makino M, Kuriyama N, Ueda Y, Nakajima K
Department of Neurology, Kyoto Prefectual University of Medicine.
Rinsho Shinkeigaku. 1998 Jul;38(7):649-52.
The patient was a 23-year-old man. He had no history of trauma in the head and neck. When he was 20 years old (in 1992), he noticed muscle atrophy and weakness in the right hand. In a hospital, he had cervical MRI study and other examinations. The diagnosis was juvenile muscular atrophy of the upper limb (Hirayama's disease). After that the symptoms became worse in the bilateral forearms and hands. The neurological examination showed severe atrophy in bilateral C7 to Th1 innervated muscles, right pyramidal sign, mild superficial and deep sensory disturbance in the dermatome of C7-Th1, and right Horner's sign. Cervical MRI and myelography revealed the atrophy of cervical cord and intraspinal cavity formations from C5 to Th1. We concluded that chronic and intermittent compression to cervical cord with flexion position made the cavities during the clinical course because these cavities were not found in the MRI taken in 1992.
患者为一名23岁男性。他无头部和颈部外伤史。20岁时（1992年），他注意到右手出现肌肉萎缩和无力。在一家医院，他接受了颈椎MRI检查及其他检查。诊断为青少年上肢肌肉萎缩症（平山病）。此后，双侧前臂和手部症状加重。神经系统检查显示双侧C7至胸1神经支配的肌肉严重萎缩，右侧锥体束征，C7 - 胸1皮节轻度浅感觉和深感觉障碍，以及右侧霍纳征。颈椎MRI和脊髓造影显示颈髓萎缩以及从C5至胸1的椎管内空洞形成。我们得出结论，在临床过程中，颈部屈曲位时对颈髓的慢性间歇性压迫导致了空洞形成，因为在1992年的MRI检查中未发现这些空洞。
