Kansu A, Girgin N, Yurdaydin C, Cetinkaya H, Uzunalimoglu O
Department of Pediatrics, School of Medicine, University of Ankara, Turkey.
Acta Paediatr Jpn. 1998 Dec;40(6):612-5. doi: 10.1111/j.1442-200x.1998.tb02001.x.
Chronic pancreatitis is a rare disease in children and is usually secondary to underlying diseases such as hereditary pancreatitis, cystic fibrosis, hyperlipidemia, prolonged malnutrition, gallstones or anomalies of the biliary-pancreatic duct system. Hereditary pancreatitis is a common cause of chronic pancreatitis in children but is often unrecognized until months or years later. We report here a family with hereditary pancreatitis in which four members are affected.
慢性胰腺炎在儿童中是一种罕见疾病,通常继发于潜在疾病,如遗传性胰腺炎、囊性纤维化、高脂血症、长期营养不良、胆结石或胆胰管系统异常。遗传性胰腺炎是儿童慢性胰腺炎的常见病因,但往往在数月或数年之后才被发现。我们在此报告一个患有遗传性胰腺炎的家族,其中四名成员受其影响。