Lo Curto F, Maraschio P, Milanesi P, Severi F, Ugazio A C, Zuffardi O
Eur J Pediatr. 1976 Nov 3;123(4):237-41. doi: 10.1007/BF00444645.
The case of a 4-month-old male with de novo partial trisomy for chromosome 14 involving the p13 leads to q24 portion is reported. He presented with growth and psychomotor retardation, peculiar facies due to nose-mouth anomalies, monolateral microphtalmia, high arched palate, and anomalies of hands and feet. These symptoms are found also in the other 8 cases of partial trisomy 14 reported in the literature. This confirms a characteristic chromosomal syndrome although the breaking points on the extra chromosome 14 are not the same in the 9 cases. The clinical picture of our case calls for careful investigations of the chronology of bone age and of the immunologic situation in further cases of total and partial trisomy 14.
本文报告了一例4个月大男性患儿,其14号染色体发生从头部分三体,涉及p13至q24区域。患儿表现为生长发育和精神运动发育迟缓,因口鼻部异常导致面容奇特,单侧小眼畸形,高拱腭,以及手足异常。文献中报道的其他8例14号染色体部分三体病例也有这些症状。这证实了一种特征性的染色体综合征,尽管9例病例中额外14号染色体上的断点并不相同。我们病例的临床表现提示,对于其他14号染色体完全三体和部分三体病例,需要仔细研究骨龄的时间顺序和免疫状况。