Skyllouriotis P, Skyllouriotis-Lazarou M, Natter S, Steiner R, Spitzauer S, Kapiotis S, Valent P, Hirschl A M, Guber S E, Laufer G, Wollenek G, Wolner E, Wimmer M, Valenta R
General & Experimental Pathology, Vienna General Hospital, University of Vienna, Medical School, Vienna, Austria.
Clin Exp Immunol. 1999 Feb;115(2):236-47. doi: 10.1046/j.1365-2249.1999.00807.x.
Studies performed in mice together with the demonstration of increased levels of heart-specific autoantibodies, cytokines and cytokine receptors in sera from cardiomyopathy (CMP) patients argued for a pathogenic role of autoimmune mechanisms in CMP. This study was designed to analyse the presence of IgG anti-heart antibodies in sera from patients suffering from hypertrophic and dilatative forms of CMP as well as from patients with ischaemic heart disease and healthy individuals. Patients' sera were analysed for IgG reactivity to Western-blotted extracts prepared from human epithelial and endothelial cells, heart and skeletal muscle specimens as well as from Streptococcus pyogenes. The IgG subclass (IgG1-4) reactivity to purified human cardiac myosin was analysed by ELISA. While sera from CMP patients and healthy individuals displayed comparable IgG reactivity to a variety of human proteins, cardiac myosin represented the prominent antigen detected strongly and preferentially by sera from CMP patients. Pronounced IgG anti-cardiac myosin reactivity was frequently found in sera from patients with dilatative CMP and reduced ventricular function. ELISA analyses revealed a prominent IgG2/IgG3 anti-cardiac myosin reactivity in CMP sera, indicating a preferential Th1-like immune response. Elevated anti-cytomegalovirus, anti-enterovirus IgG titres as well as IgG reactivity to nitrocellulose-blotted S. pyogenes proteins were also frequently observed in the group of CMP patients. If further work can support the hypothesis that autoreactivity to cardiac myosin represents a pathogenic factor in CMP, specific immunomodulation of this Th1- towards a Th2-like immune response may represent a promising therapeutic strategy for CMP.
在小鼠身上进行的研究,以及心肌病(CMP)患者血清中心脏特异性自身抗体、细胞因子和细胞因子受体水平升高的证明,都支持自身免疫机制在CMP中具有致病作用。本研究旨在分析肥厚型和扩张型CMP患者、缺血性心脏病患者以及健康个体血清中IgG抗心脏抗体的存在情况。分析了患者血清对从人上皮细胞和内皮细胞、心脏和骨骼肌标本以及化脓性链球菌制备的蛋白质免疫印迹提取物的IgG反应性。通过ELISA分析了IgG亚类(IgG1 - 4)对纯化的人心脏肌球蛋白的反应性。虽然CMP患者和健康个体的血清对多种人类蛋白质表现出相当的IgG反应性,但心脏肌球蛋白是CMP患者血清强烈且优先检测到的主要抗原。在扩张型CMP和心室功能降低的患者血清中经常发现明显的IgG抗心脏肌球蛋白反应性。ELISA分析显示CMP血清中存在显著的IgG2/IgG3抗心脏肌球蛋白反应性,表明存在优先的Th1样免疫反应。在CMP患者组中还经常观察到抗巨细胞病毒、抗肠道病毒IgG滴度升高以及对硝酸纤维素印迹的化脓性链球菌蛋白质的IgG反应性。如果进一步的研究能够支持对心脏肌球蛋白的自身反应性是CMP致病因素这一假说,那么将这种Th1样免疫反应特异性调节为Th2样免疫反应可能是CMP一种有前景的治疗策略。