de Arriba-Villamor C, Martínez-Mata A, Espinosa-Mogro H, Rubio-Viguera V
Servicio de Radiodiagnóstico, Complejo Hospitalario San Millán-San Pedro, Logroño, España.
Rev Neurol. 1998 Dec;27(160):1008-11.
Tumours of ganglion cells are very rare. They include: gangliocytoma, ganglioneuroma, Lhermitte-Duclos disease and dysembryoplastic neuroepithelial tumour. All require microscope identification of well differentiated neurons for diagnosis. Their pathogenesis is not fully understood. Some workers consider them to be dysplasias rather than true neoplasias; others refer to them as malformations.
We aim to analyze the most characteristic findings of these tumours with regard to the elements of which they are composed, their epidemiology, behavior on imaging investigations (CT and MR) and treatment.
We present two cases: one patient with a gangliocytoma and one with a ganglioglioma. Both were treated surgically, confirmed on histological study and had good clinical results.
神经节细胞瘤非常罕见。它们包括:神经节细胞瘤、神经节神经瘤、Lhermitte-Duclos病和胚胎发育不良性神经上皮肿瘤。所有这些肿瘤都需要通过显微镜鉴定分化良好的神经元来进行诊断。其发病机制尚未完全明确。一些研究者认为它们是发育异常而非真正的肿瘤;另一些人则称它们为畸形。
我们旨在分析这些肿瘤在其组成成分、流行病学、影像学检查(CT和MR)表现及治疗方面的最具特征性的发现。
我们展示两个病例:一例神经节细胞瘤患者和一例神经节胶质瘤患者。两者均接受了手术治疗,经组织学研究确诊,临床效果良好。