Sabin H I, Lidov H G, Kendall B E, Symon L
Gough-Cooper Department of Neurological Surgery, National Hospital for Nervous Diseases, London, England.
Acta Neurochir (Wien). 1988;93(3-4):149-53. doi: 10.1007/BF01402899.
A 31 year old female was admitted with a one month history of left foot drop and diplopia. CT of the posterior fossa revealed gross displacement of the 4th ventricle by a large non-enhancing cerebellar mass but gave no indication of its nature. MRI sequences showed two masses within the left cerebellar hemisphere extending into the vermis and demonstrated a very unusual septation within the lesion. In addition both cerebellar tonsils were displaced below the foramen magnum and there was a syrinx extending from C2 to the conus. At operation a demarcated lesion was excised from the apparently normal surrounding cerebellar tissue and proved histologically to be Lhermitte-Duclos disease. We believe that these are the first diagnostic magnetic resonance images of this condition.
一名31岁女性因左足下垂和复视1个月入院。后颅窝CT显示第四脑室被一个大的无强化小脑肿块明显移位，但未提示其性质。MRI序列显示左小脑半球内有两个肿块延伸至蚓部，并在病灶内显示出非常不寻常的分隔。此外，双侧小脑扁桃体均移位至枕大孔以下，并有一个从C2延伸至圆锥的空洞。手术中从看似正常的周围小脑组织中切除了一个界限清楚的病灶，组织学检查证实为Lhermitte-Duclos病。我们认为这些是该疾病的首批诊断性磁共振图像。
