一名老年男性中以低钾性麻痹为表现的干燥综合征
Hypokalaemic paralysis revealing Sjögren syndrome in an elderly man.
作者信息
al-Jubouri M A, Jones S, Macmillan R, Harris C, Griffiths R D
机构信息
Department of Chemical Pathology, Whiston Hospital, Prescot, Merseyside, UK.
出版信息
J Clin Pathol. 1999 Feb;52(2):157-8. doi: 10.1136/jcp.52.2.157.
Abstract
A 73 year old white man presented with life threatening hypokalaemic paralysis requiring admission to an intensive care unit. Biochemical investigations showed severe hypokalaemia with hyperchloraemic metabolic acidosis, a spot urine pH of 6.5, and a positive urinary anion gap, establishing the diagnosis of distal renal tubular acidosis. Autoimmune tests revealed Sjögren syndrome as the underlying cause of the distal renal tubular acidosis. Full recovery followed potassium and alkali replacement. This dramatic presentation of Sjögren syndrome has not previously been reported in an elderly man.
摘要
一名73岁白人男性因危及生命的低钾性麻痹入院，需入住重症监护病房。生化检查显示严重低钾血症伴高氯性代谢性酸中毒，随机尿pH值为6.5，尿阴离子间隙阳性，确诊为远端肾小管酸中毒。自身免疫检查显示干燥综合征是远端肾小管酸中毒的潜在病因。经补钾和补碱后完全康复。此前未见老年男性出现这种严重的干燥综合征表现的报道。
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本文引用的文献
1
Sjögren's syndrome presenting as hypokalemic paralysis due to distal renal tubular acidosis.干燥综合征表现为远端肾小管酸中毒所致的低钾性麻痹。
J Rheumatol. 1995 Dec;22(12):2366-8.
2
An unusual presentation of Sjögren's syndrome.干燥综合征的一种不寻常表现。
Clin Diagn Lab Immunol. 1996 Jul;3(4):483-4. doi: 10.1128/cdli.3.4.483-484.1996.
3
Sjögren's syndrome presenting as hypokalemic periodic paralysis.表现为低钾性周期性麻痹的干燥综合征。
Arthritis Rheum. 1993 Dec;36(12):1735-8. doi: 10.1002/art.1780361213.
4
Long-term low-dose glucocorticoid therapy associated with remission of overt renal tubular acidosis in Sjögren's syndrome.长期低剂量糖皮质激素治疗与干燥综合征中明显肾小管酸中毒的缓解相关。
Am J Med. 1985 Oct;79(4):509-14. doi: 10.1016/0002-9343(85)90040-3.
5
Hypokalemic paralysis in Sjögren's syndrome secondary to renal tubular acidosis.干燥综合征继发肾小管酸中毒所致的低钾性麻痹。
Scand J Rheumatol. 1985;14(1):58-60. doi: 10.3109/03009748509102018.
6
Hypokalemic paralysis associated with renal tubular acidosis.与肾小管酸中毒相关的低钾性麻痹。
Crit Care Med. 1987 Nov;15(11):1067-8. doi: 10.1097/00003246-198711000-00017.
7
Renal tubular acidosis in primary Sjögren's syndrome.原发性干燥综合征中的肾小管酸中毒
Clin Rheumatol. 1992 Jun;11(2):226-30. doi: 10.1007/BF02207962.
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