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Pulmonary disease severity in men with deltaF508 cystic fibrosis and residual chloride secretion.

作者信息

Thomas S R, Jaffe A, Geddes D M, Hodson M E, Alton E W

出版信息

Lancet. 1999 Mar 20;353(9157):984-5. doi: 10.1016/S0140-6736(98)05447-6.

DOI:10.1016/S0140-6736(98)05447-6
PMID:10459916
Abstract
摘要

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人鼻腔上皮的顶端 CFTR 表达与囊性纤维化的肺部疾病相关。
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